{
  "abstract": "Following Kasai portoenterostomy for biliary atresia (BA), long-term survival in children is associated with chronic liver cirrhosis leading to hepatopulmonary syndrome (HPS) and portopulmonary hypertension (PoPH). This further causes a diverse array of respiratory and circulatory symptoms. The incidence of these complications in children with BA is higher than that seen in other chronic liver diseases. With a faster progression, BA is life-threatening in some severe cases. Moreover, HPS and PoPH may coexist in the same child. Enhancing our understanding of HPS/PoPH, making an early diagnosis, rational selection of medication, and appropriate timing of liver transplantation underscore the need for multidisciplinary collaboration.",
  "authors": [
    {
      "affiliations": [
        "Department of Pediatric Surgery, Children’s Hospital of Fudan University, Shanghai, China"
      ],
      "name": "Jie Zhang"
    },
    {
      "affiliations": [
        "Department of Pediatric Surgery, Children’s Hospital of Fudan University, Shanghai, China"
      ],
      "name": "Gong Chen"
    }
  ],
  "title": "Pulmonary vascular complications in children who survive long-term after Kasai portoenterostomy for biliary atresia: a narrative review",
  "uid": "1cea715a-8811-5c32-896b-792baa3d5a07"
}