{
  "abstract": "Linear scleroderma ‘en coup de sabre’ is a rare condition characterised by inflammation and fibrosis of the skin and underlying tissues; it rarely presents in adults. The adult-onset form seldom has extracutaneous manifestations, but those that occur are usually neurological. A 43-year-old woman with epilepsy had a scar-like lesion on her forehead. The MR brain scan showed focal cortical atrophy and white matter changes on the same side as the skin lesion. Skin biopsy identified hyaline sclerosis of the reticular dermis consistent with scleroderma. Her clinical condition stabilised on mycophenolate mofetil. Although uncommon in adults, it is important to consider this rare disease in adults with scalp lesions who have epileptic seizures.",
  "authors": [
    {
      "affiliations": [
        "Neurology Department, Hospital Britanico de Buenos Aires, Buenos Aires, Argentina"
      ],
      "name": "Patxi Zavala Gottau"
    },
    {
      "affiliations": [
        "Neurology Department, Hospital Britanico de Buenos Aires, Buenos Aires, Argentina"
      ],
      "name": "Francisco Caiza-Zambrano"
    },
    {
      "affiliations": [
        "Neuroradiology Department, Hospital Británico de Buenos Aires, Buenos Aires, Argentina"
      ],
      "name": "Luis Ariel Miquelini"
    },
    {
      "affiliations": [
        "Neurology Department, Hospital Britanico de Buenos Aires, Buenos Aires, Argentina"
      ],
      "name": "Maria Sol Pacha"
    },
    {
      "affiliations": [
        "Neurology Department, Hospital Britanico de Buenos Aires, Buenos Aires, Argentina"
      ],
      "name": "Diego Tripodi"
    },
    {
      "affiliations": [
        "Neurology Department, Hospital Britanico de Buenos Aires, Buenos Aires, Argentina"
      ],
      "name": "Yemina Neme"
    },
    {
      "affiliations": [
        "Neurology Department, Hospital Britanico de Buenos Aires, Buenos Aires, Argentina"
      ],
      "name": "Mauricio Agustin Benetti"
    },
    {
      "affiliations": [
        "Neurology Department, Hospital Britanico de Buenos Aires, Buenos Aires, Argentina"
      ],
      "name": "Andrea Dolores Ezquiaga"
    },
    {
      "affiliations": [
        "Rheumathology Department, Hospital Britanico de Buenos Aires, Buenos Aires, Argentina"
      ],
      "name": "Mauricio Jiménez"
    },
    {
      "affiliations": [
        "Rheumathology Department, Hospital Britanico de Buenos Aires, Buenos Aires, Argentina"
      ],
      "name": "Andrea Gomez"
    },
    {
      "affiliations": [
        "Pathology Department, Hospital Britanico de Buenos Aires, Buenos Aires, Argentina"
      ],
      "name": "Félix Vigovich"
    },
    {
      "affiliations": [
        "Neurology Department, Hospital Britanico de Buenos Aires, Buenos Aires, Argentina"
      ],
      "name": "Oscar Adolfo Martínez"
    }
  ],
  "title": "Linear scleroderma ‘en coup de sabre’",
  "uid": "871975a9-84cc-5d62-8631-98f5498d28e2"
}
