{
  "abstract": "We present the case of a 47 year-old male with a relapsing-remitting course of large, tumefactive lesions occurring in the basal ganglia, frontal and occipital regions. In contrast to the extent of the radiological appearance, clinical symptoms remained mild during the entire illness course.Given the severity of imaging appearance and a negative extensive clinical work-up, a brain biopsy was performed, which was consistent with neuro-Behçet’s disease. Based on this, management with steroids and infliximab was initiated.Behçet’s disease is an inflammatory multisystem vasculitic condition, manifesting with mucocutaneous, ophthalmologic, arthritic, vascular and neurologic symptoms. Neurologic involvement is rare, occurring in less than 10% of cases, and tumefactive lesions are infrequently described. The heterogeneity of clinical and radiologic findings in neuro-Behçet’s disease presents a diagnostic challenge.We have reviewed the pathogenesis, clinical and radiologic features and diagnosis of neuro-Behçet’s disease, with the aim of improving recognition and early treatment of this enigmatic disorder.",
  "authors": [
    {
      "affiliations": [
        "Neurology, Princess Alexandra Hospital, Brisbane, QLD, Australia"
      ],
      "name": "Lori Mackay"
    },
    {
      "affiliations": [
        "Neurology, Princess Alexandra Hospital, Brisbane, QLD, Australia"
      ],
      "name": "Jane McAuliffe"
    },
    {
      "affiliations": [
        "Neurology, Princess Alexandra Hospital, Brisbane, QLD, Australia"
      ],
      "name": "Stefan Blum"
    }
  ],
  "title": "3699 Cascading inflammation – now you see me, now you don’t!",
  "uid": "2a445b6c-c25d-5d85-b0c6-f502422f52e0"
}