{
  "abstract": "Primary bladder perivascular epithelioid cell tumours (PEComas) are rare tumours that typically present in the third or fourth decade of life. Radiological and histopathological findings play a crucial role in establishing the diagnosis, and treatment is primarily based on surgical excision. We present the case of a primary bladder PEComa in an early adolescent male presenting with macroscopic haematuria and a hypervascular bladder mass. These peculiar symptoms should prompt consideration of the rare diagnosis of PEComa, even in paediatric patients.",
  "authors": [
    {
      "affiliations": [
        "Paediatric Surgery Unit, Université Paris-Saclay, Assistance Publique-Hôpitaux de Paris, Hopital Bicetre, Le Kremlin-Bicetre, Île-de-France, France",
        "Postgraduate school of Paediatric Surgery, University of Florence, Firenze, Italy"
      ],
      "name": "Francesca Gigola"
    },
    {
      "affiliations": [
        "Pathology department, Assistance Publique-Hôpitaux de Paris, Hopital Bicetre, Le Kremlin-Bicêtre, Île-de-France, France"
      ],
      "name": "Charlotte Mussini"
    },
    {
      "affiliations": [
        "Paediatric Surgery Unit, Université Paris-Saclay, Assistance Publique-Hôpitaux de Paris, Hopital Bicetre, Le Kremlin-Bicetre, Île-de-France, France"
      ],
      "name": "Geraldine Héry"
    },
    {
      "affiliations": [
        "Department of Pediatric and Adolescent Oncology, Gustave Roussy Cancer Campus, Université Paris-Saclay, Villejuif, France, Gustave Roussy, Villejuif, France"
      ],
      "name": "Charlotte Rigaud"
    },
    {
      "affiliations": [
        "Paediatric Surgery Unit, Université Paris-Saclay, Assistance Publique-Hôpitaux de Paris, Hopital Bicetre, Le Kremlin-Bicetre, Île-de-France, France"
      ],
      "name": "Florent Guérin"
    }
  ],
  "title": "Primary bladder perivascular epithelioid cell tumour in an early adolescent",
  "uid": "1a680ad8-df53-5f80-977c-35ca44710e46"
}
