{
  "abstract": "Pulmonary capillary haemangiomatosis (PCH) is a rare cause of pulmonary hypertension which poses a considerable diagnostic challenge. Here, we describe the case of a 14-year-old boy with gradually progressive exertional dyspnoea and cough for past 4 months. Frontal chest radiograph demonstrated prominent pulmonary artery segment with diffuse nodular opacities in bilateral lung fields ( figure 1A). CT angiography was performed to diagnose the aetiology of pulmonary artery hypertension. It revealed dilated central pulmonary arteries (figure 1B) with multiple ill-defined centrilobular nodules diffusely distributed in both lungs (figure 1C,D). No interlobular septal thickening, pulmonary thromboembolism, pleural effusion or any intracardiac/extracardiac shunt was seen. A provisional diagnosis of PCH was made which was subsequently confirmed on a lung biopsy.",
  "authors": [
    {
      "affiliations": [
        "Department of Cardiovascular Radiology & Endovascular Interventions, All India Institute of Medical Sciences, New Delhi, India"
      ],
      "name": "Arun Sharma"
    },
    {
      "affiliations": [
        "Department of Cardiovascular Radiology & Endovascular Interventions, All India Institute of Medical Sciences, New Delhi, India"
      ],
      "name": "Niraj Nirmal Pandey"
    },
    {
      "affiliations": [
        "Department of Cardiovascular Radiology & Endovascular Interventions, All India Institute of Medical Sciences, New Delhi, India"
      ],
      "name": "Sanjeev Kumar"
    }
  ],
  "title": "Pulmonary capillary haemangiomatosis causing pulmonary arterial hypertension: a clinician’s conundrum",
  "uid": "19c782b0-8ec0-5969-ae75-a92de00ef464"
}